RT Book, Section A1 Doherty, Gerard M. SR Print(0) ID 58114056 T1 Hypoplastic Left Heart Syndrome T2 Quick Answers Surgery YR 2010 FD 2010 PB The McGraw-Hill Companies PP New York, NY SN LK accesssurgery.mhmedical.com/content.aspx?aid=58114056 RD 2024/03/28 AB • An obstructive congenital heart lesion• Spectrum of underdevelopment of left-sided structures (mitral and aortic valves, left ventricle, ascending aorta, and arch)• Commonly associated with the following: -Mitral and aortic valve atresia-LV hypoplasia-Ascending aorta measures 2-3.5 mm• Coronary arteries may be stenotic• Other common anomalies: -Ventricular septal defect-Double-outlet right ventricle• 25% may have CNS anomalites• Uniformly fatal without operative treatment• Entire cardiac output delivered from right heart, maintaining oxygenation through pulmonary flow and systemic oxygen delivery• Ductus closure/inadequate interarterial communication worsens disease