RT Book, Section
A1 Blansfield, Joseph A.
A1 Libutti, Steven K.
A2 Morita, Shane Y.
A2 Dackiw, Alan P. B.
A2 Zeiger, Martha A.
SR Print(0)
ID 6164058
T1 Chapter 23. von Hippel-Lindau Disease
T2 McGraw-Hill Manual: Endocrine Surgery
YR 2010
FD 2010
PB The McGraw-Hill Companies
PP New York, NY
SN 978-0-07-160645-5
LK accesssurgery.mhmedical.com/content.aspx?aid=6164058
RD 2024/10/10
AB von  Hippel-Lindau  (VHL)  disease  is  an  autosomal  dominant  syndrome  that  predisposes  individuals  to  a  variety  of  tumors.  VHL  is  associated  with  tumors  in  a  variety  of  organs,  including  the  kidney,  adrenal  gland,  central  nervous  system  (CNS),  eye,  inner  ear,  epididymis,  and  pancreas.  VHL  is  associated  with  renal  cell  carcinoma  (RCC),  pheochromocytoma,  hemangioblastomas  of  the  CNS,  retinal  angiomas,  endolymphatic  sac  tumors,  and  pancreatic  cysts  and  solid  lesions.