RT Book, Section
A1 Dieffenbach, Bryan V.
A1 Papadakis, Konstantinos
A2 Sugarbaker, David J.
A2 Bueno, Raphael
A2 Burt, Bryan M.
A2 Groth, Shawn S.
A2 Loor, Gabriel
A2 Wolf, Andrea S.
A2 Williams, Marcia
A2 Adams, Ann
SR Print(0)
ID 1170415273
T1 Primary Repair of Pectus Excavatum
T2 Sugarbaker’s Adult Chest Surgery, 3e
YR 2020
FD 2020
PB McGraw-Hill Education
PP New York, NY
SN 9781260026931
LK accesssurgery.mhmedical.com/content.aspx?aid=1170415273
RD 2024/04/23
AB Pectus  excavatum  is  the  most  common  congenital  anterior  chest  wall  defect,  characterized  by  a  posterior  depression  of  the  sternum  and  inferior  costal  cartilages.  The  deformity  can  be  present  at  birth  or  develop  during  childhood.  The  sternal  depression  may  worsen  as  the  child  grows,  often  peaking  during  pubertal  growth.  Incidence  is  reported  in  up  to  8  per  1000  children.1,2  It  is  more  common  in  males;  the  male-to-female  ratio  is  4:1.3  The  etiology  of  the  defect  is  unknown,  although  there  is  a  suggestion  of  an  intrinsic  abnormality  of  the  costochondral  cartilage  due  to  the  occurrence  of  pectus  excavatum  in  patients  with  connective  tissue  disorders  such  as  Marfan  syndrome  and  Ehlers-Danlos  syndrome.  Scoliosis  is  present  in  up  to  20%  to  30%  of  patients  with  pectus  excavatum.3  In  addition,  a  family  history  of  pectus  excavatum  is  present  in  up  to  40%  of  patients,  suggesting  a  genetic  predisposition.  Approximately  one-third  of  all  children  with  pectus  excavatum  have  a  severe  deformity  that  warrants  evaluation  for  surgical  repair.1