TY - CHAP M1 - Book, Section TI - Porphyria, Acute A1 - Doherty, Gerard M. Y1 - 2010 N1 - T2 - Quick Answers Surgery AB - • Acute porphyrias are a group of inherited diseased that arise from errors in heme biosynthesis leading to overproduction of a porphyrin species• Acute intermittent porphyria has the most serious consequences and is the form in which patients commonly manifest an acute abdomen• Classic patient is a young woman (teens to early 20s) with an unexplained abdominal crisis• Abdominal symptoms are thought to be due to acute (abdominal visceral) autonomic dysfunction• Acute peripheral or CNS dysfunction• Recurrent psychiatric illnesses• Hyponatremia• Porphobilinogen in the urine during acute attacks SN - PB - The McGraw-Hill Companies CY - New York, NY Y2 - 2024/03/28 UR - accesssurgery.mhmedical.com/content.aspx?aid=58098425 ER -