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Chapter 17. Congenital Hearing Loss
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Which of the following is false?
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A. 50% of congenital hearing loss is secondary to environmental causes.
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B. 70% of nonsyndromic congenital hearing loss cases are inherited via an autosomal dominant pattern.
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C. 30% of syndromic congenital hearing loss cases are inherited via an autosomal recessive pattern.
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D. CMV infection is the most common infectious cause of congenital hearing loss.
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E. The vast majority of infants with CMV infection are asymptomatic.
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According to the EHDI principles, which of the following is false?
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A. All infants should be screened by 1 month of age.
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B. There are different recommended screening protocol for well-infants and NICU-infants.
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C. Diagnostic ABR is the superior audiologic screening modality.
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D. Referral for genetic testing should only be offered in select cases.
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E. Infants with confirmed hearing loss should receive intervention no later than 6 months of age.
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Match the inner ear malformation with respective name:
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Match the inner ear malformation with respective name:
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Absent interscalar septum
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Match the inner ear malformation with respective name:
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Limited cochlear duct differentiation
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Match the inner ear malformation with respective name:
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The most commonly affected protein implicated in genetic hearing loss is
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