RT Book, Section
A1 Chernoguz, Artur
A1 Frischer, Jason S.
A2 Ziegler, Moritz M.
A2 Azizkhan, Richard G.
A2 Allmen, Daniel von
A2 Weber, Thomas R.
SR Print(0)
ID 1100439662
T1 Gastrointestinal Polyps/Intestinal Cancer
T2 Operative Pediatric Surgery, 2e
YR 2014
FD 2014
PB McGraw-Hill Education
PP New York, NY
SN 978-0-07-162723-8
LK accesssurgery.mhmedical.com/content.aspx?aid=1100439662
RD 2024/04/24
AB Presence  of  colorectal  adenomas  in  children  mandates  evaluation  for  familial  polyposis  syndromes.The  first  presenting  symptoms  of  polyposis  syndromes  are  often  secondary  to  extraintestinal  manifestations  and  unrelated  to  gastrointestinal  polyps.Polyposis  syndrome  treatment  involves  a  number  of  surgical  options  which  allow  patients  to  maintain  satisfactory  lifestyles.Despite  a  number  of  surgical  options,  including  total  colectomy,  cancer  risks  remain,  and  lifetime  surveillance  is  mandatory.With  improved  survival,  surveillance  for  extraintestinal  manifestations  is  critical.Small  intestinal  malignancies  are  rare,  but  diagnosis  in  the  pediatric  population  is  often  delayed  secondary  to  low  suspicion.Colorectal  cancer  in  the  pediatric  population  is  extremely  rare,  but  children  with  polyposis  syndromes  are  at  an  extremely  high  risk  of  eventually  developing  colorectal  cancer.