RT Book, Section A1 Doherty, Gerard M. SR Print(0) ID 58105883 T1 Wilms Tumor T2 Quick Answers Surgery YR 2010 FD 2010 PB The McGraw-Hill Companies PP New York, NY SN LK accesssurgery.mhmedical.com/content.aspx?aid=58105883 RD 2024/04/20 AB • Associated with: -Beckwith-Wiedemann syndrome (macroglossia, gigantism, visceromegaly, hypoglycemia, abdominal wall defects)-WAGR syndrome (Wilms, aniridia, ambiguous genitalia, mental retardation)-Neurofibromatosis-Denys-Drash syndrome-Perlman familial nephroblastomatosis-Other genital abnormalities• 1-2% incidence of bilateral disease• As high as 7% multicentricity