TY  - CHAP
M1  - Book, Section
TI  - Tricuspid Atresia
A1  - Doherty, Gerard M.
Y1  - 2010
N1  - 
T2  - Quick Answers Surgery
AB  - •  A  congenital  heart  lesion  that  decreases  pulmonary  arterial  blood  flow  resulting  in  a  right-to-left  shunt•  Cyanosis  and  decreased  oxygen  delivery  cause  compensatory  polycythemia  (Hct  >  70%)  and  spontaneous  thrombosis•  Exercise,  acidosis,  pain  worsens  cyanosis,  can  cause  hypoxic  spells•  Squatting  increases  systemic  resistance,  causing  increased  pulmonary  flow  and  oxygen  saturation•  β-Blockers  (decreases  spasm),  fluid  intake,  HCO3  administration,  norepinephrine  (increases  systemic  resistance)  may  help  decrease  hypoxia•  Clubbing  due  to  proliferation  of  capillaries  and  AV  fistulas  in  extremities•  Bronchial  and  mediastinal  arteries  enlarge•  Ductus  arteriosus  maintains  flow  to  lungs  during  fetal  development•  Early  administration  of  alprostadil  can  allow  time  for  optimization  before  definitive  treatment•  Operative  options  to  increase  pulmonary  flow:  -Blalock-Taussig  shunt:  Subclavian  artery  to  ipsilateral  pulmonary  artery  (PA)  end  to  side  fashion-Modified  Blalock-Taussig  shunt:  Subclavian  to  PA  using  PTFE-Glenn:  Superior  vena  cava  (SVC)  to  PA  shunt-Fontan:  SVC  and  inferior  vena  cava  (IVC)  rerouted  to  PA-Excision  of  obstructive  muscle,  patch  enlargement  of  infundibulum,  and  valve  replacement  
SN  - 
PB  - The McGraw-Hill Companies
CY  - New York, NY
Y2  - 2024/04/19
UR  - accesssurgery.mhmedical.com/content.aspx?aid=58103755
ER  -